Choroid Plexus Lesions
Karen L. Salzman, MD
DIFFERENTIAL DIAGNOSIS
Common
Choroid Plexus Cyst
Enlarged Choroid Plexus
Less Common
Choroid Plexus Papilloma
Meningioma
Metastasis, Intraventricular
Ventriculitis/Plexitis
Sturge-Weber Syndrome
Neurofibromatosis Type 2
Rare but Important
Choroid Plexus Carcinoma
Lipoma
Langerhans Cell Histiocytosis
ESSENTIAL INFORMATION
Key Differential Diagnosis Issues
Most common cause of choroid plexus mass in adults is benign degenerative cyst
Helpful Clues for Common Diagnoses
Choroid Plexus Cyst
Common incidental finding in older patients (40% prevalence); bilateral
In fetus, consider trisomy 18 or 21
Enlarged Choroid Plexus
Normal in fetus, may be giant
May occur after hemispherectomy
May occur with collateral venous drainage (i.e., AVM, Sturge-Weber)
Helpful Clues for Less Common Diagnoses
Choroid Plexus Papilloma
Strongly enhancing, lobulated intraventricular mass in child
Atrium of lateral ventricle 50%, left > right
Meningioma
Solid, enhancing intraventricular mass
Origin of intraventricular location related to embryological invagination of arachnoid cells into choroid plexus
Metastasis, Intraventricular
Enhancing choroid plexus mass
Ventriculitis/Plexitis
Enhancing ependyma & choroid plexus
Ventriculomegaly with debris level
Sturge-Weber Syndrome
Enlarged, enhancing “angiomatous” ipsilateral choroid plexus
May be only finding in first 6 months
Related to abnormal fetal cortical veins
Neurofibromatosis Type 2
Extensive choroid plexus Ca++, uncommon manifestation
Helpful Clues for Rare Diagnoses
Choroid Plexus Carcinoma
Enhancing intraventricular mass & ependymal invasion
Lipoma
Extra-axial mass with fat intensity
40-50% interhemispheric fissure, may extend into choroid plexus
Langerhans Cell Histiocytosis: Rarely presents as enhancing choroid plexus massesStay updated, free articles. Join our Telegram channel
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