Marcus Gunn and Möbius Syndromes
Marcus Gunn Syndrome
Eyelid rises when mouth opens (jaw drops); lid comes down when mouth closes (jaw rises). “Jaw-winking.”
Usually accompanied by congenital unilateral ptosis. Comprises 5% of all cases of congenital ptosis. Sometimes autosomal-dominant inheritance. Presumably congenital error of neuronal wiring in brainstem. Trigeminal-oculomotor synkinesis.