Fig. 33.1
Neurophysiology: long exercise test. This shows the change in compound muscle action potential (CMAP) amplitude over 50 min following 5 min of exercise of ADM. The maximum decrement is 55 %, consistent with a positive test

Fig. 33.2

MRI thighs: (a) T1 image: this shows almost complete fatty replacement of the muscles of the posterior and medial compartment of thighs on the right and to a lesser extent on the left. The vastus lateralis muscle bilaterally as well as the inferior portion of the rectus femoris muscle on the left are also severely affected. (b) STIR image: there is a high signal indicating water deposition in the medial vastus, rectus femoris and vastus lateralis muscles bilaterally as well as the left adductor and semimembranosus muscles

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