Hemiconvulsion-Hemiplegia-Epilepsy Syndrome Alexis Arzimanoglou Charlotte Dravet Patrick Chauvel Introduction Hemiconvulsion-hemiplegia-epilepsy (HHE), described by Gastaut et al.17 in 1957, was not considered as a syndromic entity in the 1989 International League…
Epilepsy with Myoclonic Astatic Seizures Olivier Dulac Anna Kaminska Introduction Epilepsy with myoclonic–astatic seizures (EMAS) is a recently identified type of idiopathic, potentially severe epilepsy. It is characterized by a…
Idiopathic Myoclonic Epilepsy in Infancy Charlotte Dravet Federico Vigevano Introduction The syndrome of benign myoclonic epilepsy in infancy (BMEI) was not clearly identified before its first description in seven infants…
Severe Myoclonic Epilepsy in Infancy (Dravet Syndrome) Charlotte Dravet Michelle Bureau Introduction Severe myoclonic epilepsy in infancy is one of the most severe epilepsies affecting the infants and deserves to…
West Syndrome Olivier Dulac Bernardo Dalla Bernardina Catherine Chiron Introduction The occurrence of clusters of axial movements in the first year of life, combined with major and subcontinuous electroencephalographic (EEG)…
Migrating Partial Seizures In Infancy Maria Roberta Cilio Olivier Dulac Renzo Guerrini Federico Vigevano Introduction Epileptic syndromes with onset in the neonatal period or infancy with very poor prognosis have…
Benign Familial and Nonfamilial Seizures Federico Vigevano Nicola Specchio Roberto Caraballo Kazuyoshi Watanabe Introduction Benign familial and nonfamilial forms of infantile seizure and partial epilepsies of infancy are significant categories…
Overview: Syndromes of Infancy and Early Childhood Jean Aicardi Introduction The incidence of epilepsy is very high in the first years of life, reaching a peak in the first year…
Ohtahara Syndrome Shunsuke Ohtahara Yasuko Yamatogi Yoko Ohtsuka Introduction Epileptic or chronic seizures occurring during the neonatal and early infantile periods are rarely observed compared with those occurring during other…
Early Myoclonic Encephalopathy (Neonatal Myoclonic Encephalopathy) Aleksandra Djukic Federico Vigevano Perrine Plouin Solomon L. Moshé Introduction In 1978, Aicardi and Goutieres described a group of five patients with “neonatal myoclonic…
