Figure 73-1 A teased unmyelinated fiber cluster (UFC) stained with cresyl violet. The preparation allows linear measurement of internuclear lengths (upper panel). Transverse sections of a teased UFC under light…
Figure 34-1 Symmetric facial weakness and skin laxity. Her family history was significant for multiple similarly affected family members shown in the pedigree (Fig. 34-2). Her position in the pedigree…
Figure 28-1 The patient showing the kinky hair described in text. Nerve conduction studies demonstrated absent upper extremity sensory responses. The sural response was low normal amplitude (8 μV) with…
Figure 79-1 Pelvic magnetic resonance imaging scan with and without gadolinium. A, Oblique coronal T1-weighted image (T1WI) demonstrates isointense enlargement of the right S1 and S2 nerve roots. B, Fat-saturated…
Figure 80-1 Illustration of the process of amyloid specific microdissection. A, Peripheral nerve biopsy stained with Congo red indicating amyloid positive regions (arrows). B, Amyloid-positive areas are selected and outlined…
Figure 53-1 iThe extensive bleeding into sciatic nerve (A) and its multifocal distribution at different proximal to distal levels of a freshly isolated fascicle of sciatic nerve before fixation (B)…
Figure 27-1 A, Skin angiokeratoma appear as raised red lesions over the lateral flank (arrows). These are typical lesions in Fabry’s disease. B, Angiokeratomas are typically seen over pressure points,…
Figure 69-1 Chest x-ray (posteroanterior view) showing elevation of the diaphragm, right greater than left. Bilateral phrenic nerve conduction studies3 were similar at 2, 8, and 12 months. On the…
Figure 75-1 The report sheet that was completed by investigators. Participating physicians had been asked before and at the study not to discuss the approaches and criteria they planned on…
Figure 67-1 Patient with episode of erythromelalgia. Note bright red feet that have a mottled, blue or purple appearance between episodes. Also note the flushed and red appearance of ears…
